Springer Nature
13023_2019_1008_MOESM2_ESM.xlsx (21.27 kB)

Additional file 2: of Disease progression in women with X-linked adrenoleukodystrophy is slow

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posted on 2019-02-07, 05:00 authored by Irene Huffnagel, Marcel Dijkgraaf, Georges Janssens, Michel Weeghel, Björn Geel, Bwee Poll-The, Stephan Kemp, Marc Engelen
Individual clinical data: SF-36, EDSS and ALDS values. SF-36 values were compared with norm values for the Dutch population and corrected for gender and age. The SF-36 subdomain scores are expressed in Z scores, ranging from − 4 (lowest quality of life) to + 4 (highest quality of life). The SF-36 summary scores were linearly transformed to a range from 0 (lowest quality of life) to 100 (highest quality of life), with a mean of 50 and standard deviation of 10. The EDSS ranges from 0 (normal) to 10 (death). The ALDS scores are regression coefficients which were linearly transformed for interpretation, ranging from 10 (highest level of disability) to 89.47 (lowest level of disability). ALDS = AMC Linear Disability Scale; EDSS = Expanded Disability Status Scale; MCS = mental component summary; PCS = physical component summary; SF-36 = Short Form (36) Health Survey. (XLSX 21 kb)


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